BEHCET’S DISEASE [J-02]
- Idiopathic
- Recurrent
- Multisystem dis
- Young men
- HLA-B-5
- 3rd-4th decade
Presents with aphthous ulcer.
MAJOR diagnostic criteria-
1. RECURRENT APHTHOUS ULCER-
- Painful
- Shallow
- Yellowish necrotic base
2. SKIN LESIONS-
- Erythema nodosum
- Subcutaneous thrombophlebitis
- Papulo-vesicular-pustular rash
- PATHERGY TEST- on puncturing the skin with a needle, a pustule appears
- DERMATOGRAPHISM-on stroking the skin corresponding lines appear.
3. RECURRENT GENITAL ULCERATION-
Penis & scrotum- males
Labia & vagina- females
- UVEITIS-Both ant & post
MINOR Diagnostic criteria-
- ARTHRITIS- Knees, ankles, sacroiliac jts
- EPIDIDYMITIS
- INTESTINAL ULCERATION
- VASCULAR- obliterative thrombophlebitis & aneurysm
- CNS- Brainstem syn
-Meningoencephalitis
Complete Behcet;s dis- All 4 MAJOR criteria
Incomplete Behcet’s dis-
- 3 MAJOR
- 2 MAJOR + 2minor
- Uveitis + 1 MAJOR
- Uveitis + 2 minor
OCULAR-
- Episcleritis
- Keratoconjunctivitis
- Recurrent acute iritis with hypopyon
- Chr iridocyclitis
- Edema- ret, disc, macula
- Retinitis
- Periphlebitis
- Vitritis
- OA
T/T – Steroids
- Immunosuppressants
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